Complement Activation and Thrombotic Microangiopathies.
Por:
Palomo M, Blasco M, Molina P, Lozano M, Praga M, Torramade-Moix S, Martinez-Sanchez J, Cid J, Escolar G, Carreras E, Paules C, Crispi F, Quintana LF, Poch E, Rodas L, Goma E, Morelle J, Espinosa M, Morales E, Avila A, Cabello V, Ariceta G, Chocron S, Manrique J, Barros X, Martin N, Huerta A, Fraga-Rodriguez GM, Cao M, Martin M, Romera AM, Moreso F, Manonelles A, Gratacós E, Pereira A, Campistol JM and Diaz-Ricart M
Publicada:
6 dic 2019
Ahead of Print:
6 nov 2019
Resumen:
Atypical hemolytic uremic syndrome is a form of thrombotic microangiopathy caused by dysregulation of the alternative complement pathway. There is evidence showing complement activation in other thrombotic microangiopathies. The aim of this study was to evaluate complement activation in different thrombotic microangiopathies and to monitor treatment response.
Filiaciones:
Palomo M:
Josep Carreras Leukaemia Research Institute
mpalomo
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Barcelona Endothelium Team, Barcelona, Spain
Blasco M:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Group of nephro-urological diseases and renal transplantation (IDIBAPS), Barcelona, Spain
Molina P:
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Lozano M:
Apheresis Unit, Department of Hemotherapy and Hemostasis, Institut Clinic de Malalties Hematologiques i Oncologiques (ICMHO), IDIBAPS, Hospital Clinic de Barcelona, Universitat de Barcelona, Barcelona, Spain
Praga M:
Department of Nephrology, Hospital Universitario 12 de Octubre and Research Institute i+12, Madrid, Spain
Department of Medicine, Universidad Complutense, Madrid, Spain
Torramade-Moix S:
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Martinez-Sanchez J:
Josep Carreras Leukaemia Research Institute
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Barcelona Endothelium Team, Barcelona, Spain
Cid J:
Apheresis Unit, Department of Hemotherapy and Hemostasis, Institut Clinic de Malalties Hematologiques i Oncologiques (ICMHO), IDIBAPS, Hospital Clinic de Barcelona, Universitat de Barcelona, Barcelona, Spain
Escolar G:
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Carreras E:
Josep Carreras Leukaemia Research Institute
Barcelona Endothelium Team, Barcelona, Spain
:
Fetal i+D Fetal Medicine Research Center, BCNatal - Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clinic de Barcelona and Hospital Sant Joan de Deu), ICGON, IDIBAPS, Universitat de Barcelona and Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBER-ER), Barcelona, Spain
Crispi F:
Fetal i+D Fetal Medicine Research Center, BCNatal - Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clinic de Barcelona and Hospital Sant Joan de Deu), ICGON, IDIBAPS, Universitat de Barcelona and Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBER-ER), Barcelona, Spain
Quintana LF:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Group of nephro-urological diseases and renal transplantation (IDIBAPS), Barcelona, Spain
Poch E:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Group of nephro-urological diseases and renal transplantation (IDIBAPS), Barcelona, Spain
Rodas L:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Goma E:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Morelle J:
Division of Nephrology, Cliniques universitaires Saint-Luc, Institut de Recherche Expérimentale et Clinique, Université catholique de Louvain, Brussels, Belgium
Espinosa M:
Department of Nephrology, Hospital Universitario Reina Sofía e Instituto Maimonides de Investigaciones Biológicas de Córdoba (IMIBIC), Córdoba, Spain
Morales E:
Department of Nephrology, Hospital Universitario 12 de Octubre and Research Institute i+12, Madrid, Spain
Avila A:
Department of Nephrology and Renal Transplantation, Hospital Universitario Dr Peset, Valencia, Spain
Cabello V:
Department of Nephrology, Hospital Virgen del Rocio, Sevilla, Spain
Ariceta G:
Department of Pediatric Nephrology, Hospital Materno-Infantil, Vall d'Hebron, Universitat Autonoma de Barcelona, Barcelona, Spain
Chocron S:
Department of Pediatric Nephrology, Hospital Materno-Infantil, Vall d'Hebron, Universitat Autonoma de Barcelona, Barcelona, Spain
Manrique J:
Department of Nephrology, Complejo Hospitalario de Navarra, Pamplona, Spain
Barros X:
Department of Nephrology, Hospital Universitari Josep Trueta, Girona, Spain
Martin N:
Department of Nephrology, Hospital Universitari Josep Trueta, Girona, Spain
Huerta A:
Department of Nephrology, Hospital Puerta de Hierro Majadahonda, Madrid, Spain
Fraga-Rodriguez GM:
Department of Pediatric Nephrology, Hospital de la Santa Creu i Sant Pau, Universitat Autonoma de Barcelona, Barcelona, Spain
Cao M:
Department of Nephrology, Complejo Hospitalario Universitario A Coruña, Coruña, Spain
Martin M:
Department of Nephrology, Hospital Universitari Arnau de Vilanova, Lleida, Spain
Romera AM:
Department of Nephrology, Hospital General Universitario, Ciudad Real, Spain
Moreso F:
Department of Nephrology, Hospital Universitari Vall d'Hebron, Universitat Autonoma Barcelona, Barcelona, Spain
Manonelles A:
Kidney Transplant Unit, Department of Nephrology, Hospital de Bellvitge, Universitat de Barcelona, Barcelona, Spain
and
Gratacós E:
Fetal i+D Fetal Medicine Research Center, BCNatal - Barcelona Center for Maternal-Fetal and Neonatal Medicine (Hospital Clinic de Barcelona and Hospital Sant Joan de Deu), ICGON, IDIBAPS, Universitat de Barcelona and Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBER-ER), Barcelona, Spain
Pereira A:
CDB, Barcelona, Spain
Campistol JM:
Department of Nephrology and Renal Transplantation, Hospital Clinic de Barcelona, Universitat de Barcelona, Spain
Diaz-Ricart M:
Hematopathology, Department of Pathology, Centre de Diagnostic Biomedic (CDB), Hospital Clinic de Barcelona, Institut d'Investigacions Biomediques August Pi i Sunyer (IDIBAPS), Universitat de Barcelona, Barcelona, Spain
Barcelona Endothelium Team, Barcelona, Spain
Open Access
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